临床肿瘤学：病例报告

Undifferentiated embryonal sarcoma of liver in a young female:a case report and review of literature

Lekshmi R Shenoi , Ulfat Ara Wani*, Sunil K Regmi , Ajas Ibrahim , Suhail Ahmad Wani , Abrar Rasool

Undifferentiated embryonal sarcoma of liver is a rare mesenchymal malignancy, commonly occurring in children between 6 to 10 years of age. Here, we report a young female, who presented with a large liver inoperable liver mass and was clinically and radiologically a diagnostic challenge. She was histopathologically and immunohistochemically diagnosed as USEL and planned for neo- adjuvant chemotherapy, but unfortunately succumbed to toxicity in her first cycle of chemotherapy despite prudent management. Therefore, definitive diagnosis is dependent on histopathology post-biopsy or resection and prognosis on early accurate diagnosis along-with radical resection with clear margins whenever feasible. The treatment protocols are still under evaluation for standards and efficacy. Timely intervention and management of toxicities is crucial in all patients receiving chemotherapy.